Surgery is the treatment of choice with two available options. Here we present a 16yearold female with a fibrous dysplasia in the maxilla. Fibrous dysplasia of the mandible pdf free download. It represents with three forms namely monostotic single bone involvement, polyostotic multiple bone. Orbital scoringtransposition supraorbital fibrous dysplasia dr. Fibrous dysplasia of the maxilla jama otolaryngology. Pdf radiographic diagnosis of fibrous dysplasia in maxilla. Fibrous dysplasialike appearance of the frontal process. Craniofacial fibrous dysplasia is 1 of 3 types of fibrous dysplasia that can affect the bones of the craniofacial complex, including the mandible and maxilla. Fibrous dysplasia is a nonneoplastic developmental disease of bone, which manifest as a defect in osteoblastic differentiation and maturation. Pdf fibrous dysplasia is a rare bone disorder characterized by the replacement of normal bone by abnormal fibrous tissue.
Fibrous dysplasia is a rare bone disorder characterized by the replacement of normal bone by abnormal fibrous tissue. Fibrous dysplasia of the mandible fibrous dysplasia report george w. The purpose of this study was to determine its prevalence and findings on ct. Cone beam computed tomography scan revealed a mixed radiopacity that extended from the alveolar crest of the right posterior teeth to the right orbital. Fibrous dysplasia is a developmental tumor like condition in which normal bone is replaced by excessive proliferation of cellular fibrous connective tissue intermixed with irregular bony trabeculae. Radiographic diagnosis of fibrous dysplasia in maxilla. The maxilla is the most commonly affected facial bone, with facial asymmetry being the usual complaint. The etiology of fibrous dysplasia has been linked to an activating mutation in the gene that encodes the.
Fibrous dysplasia is a common benign skeletal lesion that may involve one bone monostotic or multiple bones polyostotic and occurs throughout the skeleton with a predilection for the long bones, ribs, and craniofacial bones. A retrospective study of consecutive paranasal sinus ct scans was preformed on outpatients without a history of trauma or previous surgery in our hospital during 6 months. Here we present a 16yearold female with a fibrous dysplasia in the maxilla and obliteration of the sinus in the same side. It is seen in 2 main forms of presentation, monoostotic and the polyostotic form with cafe au lait spots and precocious puberty mccunealbright. The frontal process of the maxilla occasionally shows a localized fdlike appearance. Fibrous dysplasia is characterized by excessive proliferation of boneforming mesenchymal cells.
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